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The May-Hegglin anomaly(MHA) is a rare autosomal dominant disorder. This is the most common type of hereditry or inherited giant platelet disorders(lGPDs). It is characterized by the presence of giant platelets, thrombocytopenia, abnormal bluish inclusions in the granulocytes, and mild bleeding symptoms. The mechanism of the hemostatic defect is not entirely clear, but bleeding is proportional to the degree of thrombocytopenia. We experienced the mother and neonate affected With May-Hegglin anomaly. In the peripheral blood smear, giant platelets and light blue basophilic inclusion bodies in the granulocytes are observed.



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May-Hegglin anomaly, Giant platelet, Thrombocytopenia