초록 열기/닫기 버튼
AOSD는 다양한 중증도의 임상증상을 보이는 드문 질환으로 급성 간부전이 동반되는 경우는 드물지만 사망률이 높은 만큼 신속한 진단과 적절한 치료가 무엇보다 중요하다. 저자들은 스테로이드로 성공적으로 치료한 급성 열성 간염을 동반한 AOSD 1예를 경험하였기에 보고하는 바이다.
Adult-onset Still’s Disease (AOSD) is a rare, immune-mediated, multisystem inflammatory disorder characterized by quotidian spiking fevers, an evanescent rash, arthritis, lymphadenopathy, splenomegaly, a sore throat, leukocytosis, and liver dysfunction. Its clinical manifestations are very diverse, from relatively mild symptoms to severe complications, such as disseminated intravascular coagulation, cardiac tamponade, acute respiratory distress syndrome, hemophagocytic syndrome, and hepatic failure. Hepatic failure is an extremely rare complication that could lead to death. Therefore, early diagnosis and treatment are important. We report a case of adult-onset Still’s disease with acute febrile hepatitis. (Korean J Med 2011;80:620-624)
키워드열기/닫기 버튼
Hepatitis; Adult-onset Still’s disease
